THE IMPORTANCE OF PREVENTIVE DENTAL HEALTH CARE IN CHILDREN WITH RARE DISEASES
Keywords:
rare disease,, children, oral health, preventive dental careAbstract
Rare diseases are chronic, life-threatening conditions that affect fewer than 5 people out of every 10,000. They involve an extremely heterogeneous group of progressive and degenerative diseases. Each of them has a distinct clinical manifestation which may include anatomical, physiological and/or neurological disorders and it can also be accompanied by changes in different parts of the body. Over 7000 rare diseases have been identified with orofacial anomalies accounting for about 15% of them. The first symptoms usually appear during the earliest childhood. In most cases, accurate diagnosis of rare diseases requires a long period of time. Consequently, therapy is complex and requires a multidisciplinary approach.
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